67例儿童先天性肺囊性病变影像学特征

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摘要目的：总结67例儿童先天性肺囊性病变影像学特征，为临床早期正确诊断先天性肺囊性病变提供依据。方法：选择温州医科大学附属第二医院育英儿童医院2000年1月至2016年1月收治的67例先天性肺囊性病变患儿作为研究对象，分析患儿临床资料，总结其临床、影像学表现。结果：支气管源性囊肿影像学表现为单发囊肿29例，多发囊肿13例，表现为圆形或类圆形，边界清楚，囊内表现为空洞、液性、气液性，囊壁厚薄不一。先天性肺囊性腺瘤样畸形表现为单侧肺部一叶或多叶多发气囊肿8例，肺部高密度影4例，左肺下叶巨大液气囊肿1例。肺隔离症影像学可见胸腔内扩张肠管与腹腔肠管相延续，健侧肺脏受压明显，另有3例见肺部高密度影，可见多个囊状或蜂窝状透亮影，1例CTA提示左下肺动静脉瘘，1例病变位于左肺下叶，呈蜂窝状囊状改变。结论：先天性肺囊性病变临床表现及体征无明显特异性，若影像学上表现为单发或多发空洞、液性、气液性囊肿需要考虑该疾病的可能。

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关键词 ：先天性肺囊性病变, 支气管源性囊肿, 先天性肺囊性腺瘤样畸形, 先天性大叶性肺气肿, 肺隔离症

Abstract：Objective: To summarize the imaging features of 67 cases of children’s congenital cystic lung lesions, so as to diagnosis these disease timely. Methods: Sixty seven cases of congenital cystic lung lesions children were collected in the Second Affiliated Hospital & Yuying Children’s Hospital of Wenzhou Medical University from January 2000 to January 2016. The clinical data and imaging findings were retrospectively analyzed. Results: For patients of bronchogenic cyst, 29 cases showed solitary cyst, 13 cases were found with multiple systs. For patients of congenital cystic adenomatoid malformation, 8 cases were found multiple air syst in unilateral single or multiple lung lobe, 4 cases were showed pulmonary high density shadow, 1 cases were found huge liquid-gas syst in left lower lobe. For patients of pulmonary sequestration, 3 cases were found of pulmonary high density shadow, 1 cases of CTA showed pulmonary arterio-venous fistula, 1 cases of CTA were showed honeycomb cystic in lower lobe of left lung. Conclusion: There are no specific manifestations and signs in patient with congenital cystic lung lesions. If the imaging performance are solitary or multiple cavities, liquid, or gas-liquid cyst, the possibility of congenital cystic lung lesions may need to be considered.

Key words： congenital cystic lung lesions bronchogenic cyst congenital cystic adenomatoid malformation congenital lobar emphysema pulmonary sequestration

收稿日期: 2017-03-08

作者简介: 项蔷薇（1980-），女，浙江苍南人，主治医师，硕士。

链接本文:

https://xb.wmu.edu.cn/CN/ 或 https://xb.wmu.edu.cn/CN/Y2017/V47/I11/836

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